Early onset of a nasal perivascular epithelioid cell neoplasm not related to tuberous sclerosis complex

نویسندگان

  • S. GANA
  • P. MORBINI
  • G. GIOURGOS
  • E. MATTI
  • F. CHU
  • C. DANESINO
  • F. PAGELLA
چکیده

Perivascular epithelioid cell neoplasms are a group of rare tumours reported in various organs under a variety of designations. Such tumours are of interest primarily because of the distinctive morphology of their cell population and their immunoreactivity with melanocytic and myoid markers. There is a strong association between perivascular epithelioid cell neoplasms and tuberous sclerosis complex. Perivascular epithelioid cell neoplasms very rarely occur in the upper aero-digestive tract. To date only three cases of nasal perivascular epithelioid cell neoplasms have been reported in the literature. The present report refers to a 22-year old woman, without any stigmata of tuberous sclerosis complex, with early onset of a polypoid nasal mass with pathological and immunohistochemical features entirely compatible with those of a perivascular epithelioid cell neoplasm.

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عنوان ژورنال:

دوره 32  شماره 

صفحات  -

تاریخ انتشار 2012